Topography of FUS pathology distinguishes late-onset BIBD from aFTLD-U
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چکیده
منابع مشابه
Topography of FUS pathology distinguishes late-onset BIBD from aFTLD-U
BACKGROUND Multiple neurodegenerative diseases are characterized by the abnormal accumulation of FUS protein including various subtypes of frontotemporal lobar degeneration with FUS inclusions (FTLD-FUS). These subtypes include atypical frontotemporal lobar degeneration with ubiquitin-positive inclusions (aFTLD-U), basophilic inclusion body disease (BIBD) and neuronal intermediate filament incl...
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ژورنال
عنوان ژورنال: Acta Neuropathologica Communications
سال: 2013
ISSN: 2051-5960
DOI: 10.1186/2051-5960-1-9